{"global_stoichiometry": "Homo 5-mer - A5 ", "ligstr": "", "uniprot_ac": "", "inchi": "", "reference": "Nat Commun. 2019 Mar 20;10(1):1269.", "author": "Swuec, P., Lavatelli, F., Tasaki, M., Paissoni, C., Rognoni, P., Maritan, M., Brambilla, F., Milani, P., Mauri, P., Camilloni, C., Palladini, G., Merlini, G., Ricagno, S., Bolognesi, M.", "type": "Fibril", "ligand_id": "", "species": "Homo sapiens", "method": "ELECTRON MICROSCOPY", "keyword": "Monoclonal immunoglobulin light chains (LC)", "gene_names": "", "chain_id": "", "ligand_mw": "", "inchi_key": "", "secondary_structure": "NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT#CEEEECSSEEEECSSCCEEECCCCEEEEESCEEEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCEEEEEEECCCEEEEEEEEEEEEEEEEEECSEEESCEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCCC&NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT#CEEEECSSEEEECSSCCEEECCCCEEEEESCEEEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCEEEEEEECCCEEEEEEEEEEEEEEEEEECSEEESCEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCCC&NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT#CEEEECSSEEEECSSCCEEEECCCEEECSSCEEEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCEEEEEEECCCEEEEEEEEEEEEEEEEEECSEEESCEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCCC&NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT#CEEEECSSEEEECSSCCEEEECCCEEECSSCEEEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCEEEEEEECCCEEEEEEEEEEEEEEEEEECSEEESCEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCCC&NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT#CEEEECSSEEEECSSCCEEECCCCEEECSSCEEEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCEEEEEEECCCEEEEEEEEEEEEEEEEEECSEEESCEEECCCCCCCCCCCCCCCCCCCCCCCCCCCCCCCC", "amyloid_non_amyloid": "Amyloid", "length": "136", "remarks": "Cryo-EM structure of cardiac amyloid fibrils from an immunoglobulin light chain (AL) amyloidosis patient.", "protein_name": "Immunoglobulin Light-Chain", "peptide_protein_sequence": "chain-ID A: NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT; chain-ID B: NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT; chain-ID C: NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT; chain-ID D: NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT; chain-ID E: NFMLTQPHSVSESPGKTLTISCTGSSASIASHYVQWYQQRPGGAPTTLIYENDQRPSEVPDRFSGSIDSSSNSASLTISGLKTEDEADYYCQSYDGNNHWVFGGGTKLTVLSQPKAAPSVTLFPPSSEELQANKAT", "ligand_name": "", "ligand_smiles": "", "pdb_id": "6HUD", "ec_number": "", "pdb_classification": "PROTEIN FIBRIL", "mutation_s_field": "No", "ligand_formula": "", "r_value_free": "", "alternative_name": "", "description": "The cryo-electron microscopy map and molecular model of amyloid fibrils extracted from the heart of an AL amyloidosis patient with severe amyloid cardiomyopathy. The helical fibrils are composed of a single protofilament, showing typical stacking and cross-Beta architecture. ", "resolution": "4.0", "pmid": "30894521", "entry": "S-0554"}